Periodic Paralyses (HypoPP, NormoPP, HyperPP and ATS)
Version 2: Oct 2015 Translated into English for the Periodic Paralysis Association
Author: Bas Stunnenberg, MD/ PhD-candidate, resident Neurology, Radboud University Medical Center Nijmegen, Netherlands
Instructions:Example: You (a HypoPP patient) wake up in the morning (8 am) of Januari 1 2016 with an attacks of muscle weakness of the arms and legs. The evening before the attack you had a big meal of carbohydrates and went to the gym. The attack duration (of subjective muscle weakness) is 2 hours and you need assistance to get to the toilet and get dressed and you can not walk without assitance. During the attack you take 120 ml (mmol) of KCl.
|Attack date||Attack duration (min)||Attack severity (see Attack severity)||Triggering factors||Attack Medication taken during attack||Muscles involved during the attacks (arms / legs/ face/ all)|
|1-1-2016||120||4||Carbohydrate-rich meal, (rest after) exercise||120 ml KCl||Legs and arms|
Attack severity can be scored using the GBS-severity scale that was also used in the previous treatment studies on the group level (Tawil et al. Annals of Neurology, 2000).
Attack severity is scored on a 1-6 scale with: 1= no complaints, 2= mild complaints of muscle weakness but capable of performing daily tasks, 3= capable of walking without help of a walking stick, but not capable of performing daily tasks, 4= Only capable of walking with a walking stick or with support of another person, 5= Bound to bed or wheelchair due to the attack of weakness, 6= ER or ICU admission due to severe weakness paralysis of arms and legs.
For multiple attacks on one day use multiple lanes to record the attack characteristics.
Period (duration 1 month): from _____ till _____ .